Mayer-Rokitansky-Kuster-Hauser (MRKH) Syndrome in a Child with Idiopathic Precocious Puberty
Annals of Pediatric Endocrinology & Metabolism
;
: 126-129, 2012.
Article
Dans Coréen
| WPRIM
| ID: wpr-138738
ABSTRACT
Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is a rare congenital disorder characterized by the congenital absence or hypoplasia of the uterus and the upper two thirds of the vagina due to mullerian duct malformation during embryogenesis. MRKH syndrome usually presents as primary amenorrhea in adolescence in females showing normal development of secondary sexual characteristics and a normal 46, XX karyotype. For this reason, MRKH syndrome usually remains undiagnosed until primary amenorrhea or difficulty in sexual intercourse occurs. In this study, a case of MRKH syndrome diagnosed in a child with idiopathic precocious puberty is reported.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Puberté précoce
/
Rachis
/
Utérus
/
Vagin
/
Malformations multiples
/
Coït
/
Somites
/
Développement embryonnaire
/
Caryotype
/
Aménorrhée
Limites du sujet:
Adolescent
/
Enfant
/
Femelle
/
Humains
/
Grossesse
langue:
Coréen
Texte intégral:
Annals of Pediatric Endocrinology & Metabolism
Année:
2012
Type:
Article
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