Familial gigantiform cementoma / 대한구강악안면방사선학회지
Korean Journal of Oral and Maxillofacial Radiology
;
: 157-162, 2006.
Article
Dans Coréen
| WPRIM
| ID: wpr-155918
ABSTRACT
Familial gigantiform cementoma is a rare fibro-cemento-osseous disease of the jaws which appears to be transmitted as an autosomal dominant trait with variable expressivity of the phenotype. A 7-year-old girl visited DKUDH complaining of the painless facial deformity. Clinically, significant facio-lingual expansion was observed at the left maxilla, left mandibular body and symphysis portion. Malposition of lower anterior teeth was found. Panoramic radiograph and CT scan showed the extensive expansile mixed lesion at maxilla and mandible. Bone scan revealed hot spot at the maxilla and left side of mandible. Histologic examination revealed moderately dense fibrous connective tissue with scattered masses resembling cementum. The patient's mother had a history of the mandibular resection due to benign tumor. Her younger brother had buccal expansion of right mandible. We report our finding of a family that has exhibited clinical, radiographic and histologic findings consistent with the familial gigantiform cementoma.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Phénotype
/
Malformations
/
Dent
/
Cémentome
/
Tumeurs odontogènes
/
Tomodensitométrie
/
Tissu conjonctif
/
Cément dentaire
/
Fratrie
/
Mâchoire
Limites du sujet:
Enfant
/
Femelle
/
Humains
langue:
Coréen
Texte intégral:
Korean Journal of Oral and Maxillofacial Radiology
Année:
2006
Type:
Article
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