Single Lung Transplantation in the Patient with End-stage Lymphangioleiomyomatosis: Report of 1 case / 대한흉부외과학회지
The Korean Journal of Thoracic and Cardiovascular Surgery
;
: 1015-1018, 2004.
Article
Dans Coréen
| WPRIM
| ID: wpr-158779
ABSTRACT
Lymphangioleiomyomatosis (LAM) is a rare disease in women in childbearing age leading to progressive respiratory failure. LAM is characterized by an abnormal harmartomatous proliferation of smooth muscle cells surrounding the blood vessels, lymphatics and airways in the lung. This proliferation leads to airway obstruction, cystic alveolar change and lymphatic obstruction. Patients present with dyspnea, pneumothorax, cough, chest pain, hemoptysis, and chylous effusion. Although lung transplantation is the only therapeutic modality in end-stage LAM with respiratory failure, there has not been any report of successful treatment in Korea. We report one case of successful left single lung transplantation in a 40 year old woman suffering from end-stage LAM.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Pneumothorax
/
Insuffisance respiratoire
/
Vaisseaux sanguins
/
Douleur thoracique
/
Transplantation pulmonaire
/
Lymphangioléiomyomatose
/
Toux
/
Myocytes du muscle lisse
/
Maladies rares
/
Obstruction des voies aériennes
Limites du sujet:
Adulte
/
Femelle
/
Humains
Pays comme sujet:
Asie
langue:
Coréen
Texte intégral:
The Korean Journal of Thoracic and Cardiovascular Surgery
Année:
2004
Type:
Article
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