An Atypical Giant Angiomyxoma with Multiple Superficial Angiomyxomas / 대한피부과학회지

ABSTRACT

Superficial angiomyxoma (SAM), often referred to as cutaneous myxoma, is a rare benign myxoid tumor of soft tissue. It commonly manifests as a single mass, but is occasionally detected as multiple tumors in Carney's complex. Nowadays, however, SAM is regarded as an independent cutaneous tumor regardless of whether Carney's complex is present. SAM occurs most commonly on the trunk, limbs, head, and neck. Herein we report a rare case involving a 21-year-old woman who presented with multiple tumors consisting of a single giant pedunculated mass surrounded by multiple nodules on her left labium major. Histological analysis revealed that the tumors were composed of widely scattered bland spindle-shaped or stellate cells with ill-defined cytoplasm and variably sized vessels within a basophilic myxoid stroma. The tumors were completely removed by total excision and primary closure with an excellent cosmetic outcome.