Ewing's Sarcoma/Peripheral Primitive Neuroectodermal Tumor in the Cerebellopontine Angle : Diagnosis and Treatment
Journal of Korean Neurosurgical Society
; : 359-362, 2011.
Article
de En
| WPRIM
| ID: wpr-188482
Bibliothèque responsable:
WPRO
ABSTRACT
Ewing's sarcoma/primitive neuroectodermal tumor (ES/PNET) is an unusual malignancy with aggressive behavior. ES/PNET in the cerebellopontine angle (CPA) is extremely uncommon, and we report on a rare case here. A 31-year-old man presented with one month history of left facial palsy, hearing loss, swallowing difficulty, and hoarseness. Magnetic resonance images showed a large mass in the left CPA and a small one in the right cerebellar hemisphere. The patient underwent a surgery for the CPA mass lesion, and the pathology was compatible with ES/PNET. Radiation therapy and chemotherapy were administered. In contrast to the initial radiologic findings resembling vestibular schwannoma or meningioma, ES/PNET had several distinct clinical features. A patient with a CPA mass and presenting unusual clinical features should be suspected of having a rare malignancy.
Mots clés
Texte intégral:
1
Indice:
WPRIM
Sujet Principal:
Sarcome d'Ewing
/
Spectroscopie par résonance magnétique
/
Enrouement
/
Neurinome de l'acoustique
/
Angle pontocérébelleux
/
Tumeurs neuroectodermiques
/
Tumeurs neuroectodermiques primitives
/
Déglutition
/
Paralysie faciale
/
Perte d'audition
Type d'étude:
Diagnostic_studies
Limites du sujet:
Adult
/
Humans
langue:
En
Texte intégral:
Journal of Korean Neurosurgical Society
Année:
2011
Type:
Article