Beckwith-Wiedemann sydrome with left adrenal cortical neoplasm
Journal of the Korean Association of Pediatric Surgeons
;
: 160-165, 2000.
Article
Dans Coréen
| WPRIM
| ID: wpr-189793
ABSTRACT
Beckwith-Wiedemann sydrome is a multisystemic pattern of congenital anomalies with overgrowth. This syndrome is first described independently by Beckwith in 1963 and by Wiedemann in 1964. There is wide spectrum of clinical manifestations, including prenatal or postnatal overgrowth, neonatal hypoglycemia, macroglossia, visceromegaly, omphalocele, hemihypertrophy and a predisposition for embryonal tumors, most frequently Wilms' tumor. We experienced a case of Beckwith-Wiedemann syndrome who developed left adrenal cortical neoplasm of indeterminate malignant potential.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Syndrome de Beckwith-Wiedemann
/
Tumeur de Wilms
/
Hernie ombilicale
/
Hypoglycémie
/
Macroglossie
langue:
Coréen
Texte intégral:
Journal of the Korean Association of Pediatric Surgeons
Année:
2000
Type:
Article
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