The Management of Cardiovascular Abnormalities in Patient With LEOPARD Syndrome
Korean Circulation Journal
;
: 339-342, 2010.
Article
Dans Anglais
| WPRIM
| ID: wpr-196627
ABSTRACT
LEOPARD syndrome (LS) is a rare hereditary disorder in Asian countries. This syndrome consists of multiple systemic abnormalities. In particular, characteristic cardiovascular effects in LS may include variable clinical manifestations from benign to life-threatening courses. The cardiac effects of this syndrome consist of left ventricular hypertrophy (LVH), pulmonary stenosis (PS), coronary artery dilatation and electrocardiogram(ECG) abnormalities. Since there are few LS patients who have undergone a complete cardiovascular evaluation, the nature and clinical prognosis of cardiovascular abnormalities in this syndrome remain uncertain. Also, there have been few reports on therapeutic strategies for cardiovascular abnormalities in LS. Here we describe a case of LS who presented with multiple cardiovascular problems and underwent successful surgical and medical treatment.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Pronostic
/
Sténose de la valve pulmonaire
/
Hypertrophie ventriculaire gauche
/
Malformations cardiovasculaires
/
Vaisseaux coronaires
/
Syndrome LEOPARD
/
Asiatiques
/
Panthera
/
Dilatation
/
Lentigo
Type d'étude:
Étude pronostique
Limites du sujet:
Humains
langue:
Anglais
Texte intégral:
Korean Circulation Journal
Année:
2010
Type:
Article
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