Parry-Romberg Syndrome with En Coup de Sabre
Annals of Dermatology
; : 342-347, 2011.
Article
de En
| WPRIM
| ID: wpr-204013
Bibliothèque responsable:
WPRO
ABSTRACT
Parry-Romberg syndrome (PRS) is a relatively rare degenerative disorder that is poorly understood. PRS is characterized by slowly progressing atrophy affecting one side of the face, and is frequently associated with localized scleroderma, especially linear scleroderma, which is known as en coup de sabre. This is a report of the author's experiences with PRS accompanying en coup de sabre, and a review of the ongoing considerable debate associated with these two entities. Case 1 was a 37-year-old woman who had right hemifacial atrophy with unilateral en coup de sabre for seven years. Fat grafting to her atrophic lip had been conducted, and steroid injection had been performed on the indurated plaque of the forehead. Case 2 was a 29-year-old woman who had suffered from right hemifacial atrophy and bilateral en coup de sabre for 18 years. Surgical corrections such as scapular osteocutaneous flap and mandible/maxilla distraction showed unsatisfying results.
Mots clés
Texte intégral:
1
Indice:
WPRIM
Sujet Principal:
Atrophie
/
Sclérodermie localisée
/
Transplants
/
Hémiatrophie faciale
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Front
/
Lèvre
Limites du sujet:
Adult
/
Female
/
Humans
langue:
En
Texte intégral:
Annals of Dermatology
Année:
2011
Type:
Article