Three-year Follow-up of Niemann-Pick Disease with Pulmonary Involvement: A Case Report
Journal of the Korean Radiological Society
; : 37-40, 2005.
Article
Dans Ko
| WPRIM
| ID: wpr-27870
Responsable en Bibliothèque :
WPRO
ABSTRACT
Niemann-Pick disease is a rare inherited metabolic storage disease that causes excessive intracellular storage of sphingomyelin in various organs. We present the pulmonary imaging findings with particular emphasis on the CT findings in a case of Niemann-Pick disease type B with pulmonary involvement. The chest radiograph showed fine reticulonodular opacities in both basal lung fields, and the high-resolution chest CT showed centrilobular nodular opacities and smooth thickening of the interlobar fissure and interlobular septum with a basal lung predominance. Coronal reformatted CT revealed a prominent interlobular septal thickening around the diaphragm. The follow-up high-resolution chest CT showed no significant interval changes over a 3-years period.
Texte intégral:
1
Indice:
WPRIM
Sujet Principal:
Muscle diaphragme
/
Radiographie thoracique
/
Tomodensitométrie
/
Maladies de Niemann-Pick
/
Études de suivi
/
Poumon
Type d'étude:
Observational_studies
/
Prognostic_studies
langue:
Ko
Texte intégral:
Journal of the Korean Radiological Society
Année:
2005
Type:
Article