Hereditary Sclerosing Poikiloderma
Journal of Korean Medical Science
;
: 225-227, 2012.
Article
Dans Anglais
| WPRIM
| ID: wpr-33789
ABSTRACT
Hereditary sclerosing poikiloderma (HSP) is a very rare disease. The clinical features are principally widespread poikiloderma and linear hyperkeratotic and sclerotic bands. We report an 18-yr-old male who presented reticular hyperpigmented lesions on the trunk and extremities since 2-yr-old. Also, linear sclerosing bands appeared on both antecubital and popliteal fossae after yr. Histopathologic finding showed dense sclerotic collagen fibers with telangiectasia in the upper dermis and fragmentations of damaged elastic fibers in the elastic stain, consistent with HSP. We report the first Korean case of HSP.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Syndrome de Rothmund-Thomson
/
Sclérose
/
Maladies de la peau
/
Malformations multiples
/
Hyperpigmentation
/
Tissu élastique
/
Doigts
/
Micrognathisme
Limites du sujet:
Adolescent
/
Humains
/
Mâle
langue:
Anglais
Texte intégral:
Journal of Korean Medical Science
Année:
2012
Type:
Article
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