Early-onset Childhood Sarcoidosis with Incidental Multiple Enchondromatosis
Journal of Korean Medical Science
;
: 96-100, 2012.
Article
Dans Anglais
| WPRIM
| ID: wpr-39059
ABSTRACT
The triad of rash, arthritis, and uveitis seems to be characteristic for early-onset childhood sarcoidosis. We describe an interesting case of early-onset childhood sarcoidosis coexisting enchondromatosis, which clinically masquerade as Langerhans cell histiocytosis. A 33 months old girl presented with skin rash, subcutaneous nodules with polyarthritis, and revealed the involvement of lymph nodes as well as spleen during work-up. She also presented with multiple osteolytic lesions which pathologically proven enchondromatosis. Oral prednisone was prescribed at 2 mg/kg/day for 2 months until when subcutaneous nodules and joint swellings almost disappeared, and then slowly tapered over a period of 5 months. We report an unusual case of early-onset childhood sarcoidosis presented with osteolytic bone lesions which were irrelevant to sarcoidosis.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Arthrite
/
Sarcoïdose
/
Prednisone
/
Administration par voie orale
/
Diagnostic différentiel
/
Enchondromatose
/
Imagerie du corps entier
/
Exanthème
/
Tomographie par émission de positons couplée à la tomodensitométrie
/
Anti-inflammatoires
Type d'étude:
Etude diagnostique
Limites du sujet:
Enfant d'âge préscolaire
/
Femelle
/
Humains
langue:
Anglais
Texte intégral:
Journal of Korean Medical Science
Année:
2012
Type:
Article
Documents relatifs à ce sujet
MEDLINE
...
LILACS
LIS