Early-onset Childhood Sarcoidosis with Incidental Multiple Enchondromatosis
Journal of Korean Medical Science
; : 96-100, 2012.
Article
de En
| WPRIM
| ID: wpr-39059
Bibliothèque responsable:
WPRO
ABSTRACT
The triad of rash, arthritis, and uveitis seems to be characteristic for early-onset childhood sarcoidosis. We describe an interesting case of early-onset childhood sarcoidosis coexisting enchondromatosis, which clinically masquerade as Langerhans cell histiocytosis. A 33 months old girl presented with skin rash, subcutaneous nodules with polyarthritis, and revealed the involvement of lymph nodes as well as spleen during work-up. She also presented with multiple osteolytic lesions which pathologically proven enchondromatosis. Oral prednisone was prescribed at 2 mg/kg/day for 2 months until when subcutaneous nodules and joint swellings almost disappeared, and then slowly tapered over a period of 5 months. We report an unusual case of early-onset childhood sarcoidosis presented with osteolytic bone lesions which were irrelevant to sarcoidosis.
Mots clés
Texte intégral:
1
Indice:
WPRIM
Sujet Principal:
Arthrite
/
Sarcoïdose
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Prednisone
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Administration par voie orale
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Diagnostic différentiel
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Enchondromatose
/
Imagerie du corps entier
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Exanthème
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Tomographie par émission de positons couplée à la tomodensitométrie
/
Anti-inflammatoires
Type d'étude:
Diagnostic_studies
Limites du sujet:
Child, preschool
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Female
/
Humans
langue:
En
Texte intégral:
Journal of Korean Medical Science
Année:
2012
Type:
Article