Anomalous Scleral Insertion of Superior Oblique in Axenfeld-Rieger Syndrome
Korean Journal of Ophthalmology
;
: 62-64, 2009.
Article
Dans Anglais
| WPRIM
| ID: wpr-39304
ABSTRACT
Axenfeld-Rieger syndrome (ARS) is associated with ocular and systemic anomalies. PITX2 is known to be a major controlling gene in the pathogenesis of ARS and is associated with differentiation in both the neural crest and mesoderm during eye development. A 4-year-old girl with bilateral ARS had 20 prism diopters (PD) of exotropia with 30PD of A- pattern deviation, more than 20PD of dissociated vertical deviation (DVD), and severe superior oblique overaction (SOOA). During surgery we observed that the SO inserted more posteriorly than normal. We believe this finding is one of the abnormal manifestations of the development of the extraocular muscles in ARS.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Nerf optique
/
Complications postopératoires
/
Sclère
/
Procédures de chirurgie ophtalmologique
/
Syndrome
/
Malformations dentaires
/
Malformations multiples
/
Malformations oculaires
/
Études de suivi
/
Mouvements oculaires
Type d'étude:
Étude observationnelle
/
Étude pronostique
Limites du sujet:
Enfant d'âge préscolaire
/
Femelle
/
Humains
langue:
Anglais
Texte intégral:
Korean Journal of Ophthalmology
Année:
2009
Type:
Article
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