A Case of Unilateral Retinitis Pigmentosa

ABSTRACT

Retinitis pigmentosa has been recognized as a symmetrical, bilateral, hereditary, tapetoretinal degeneration with night blindness, visual field loss, and abnormal ERG. Unilateral retinitis pigmentosa is a rather rare disease. Pedraglia described first reported a case of suspected unilateral retinitis pigmentosa in 1865. Francois and Verriest proposed the following four criteria of the unilateral retinitis pigmentosa the presence of functional changes ophthalmoscopically typical primary pigmentary degeneration in the affected eye, the absence of a tapetoretinal dystrophy in the fellow eye with normal ERG over five years and exclusion of the inflammatory cause in the affected eye. We report a case of unilateral retinitis pigmentosa in 29 year-old female who has been followed for over five years.