Renal and hepatic angiomyolipoma and renal failure in two cases of tuberous sclerosis / 대한피부과학회지

ABSTRACT

The abdominal manifestations of tuberous sclerosis are most frequently related to hamartomas of the kidneys which are readily detectable on CT scans because of their fat content. However, lipomas or angiomyolipomas of the liver are quite rare. Two patients with angiomyolipomas of the kidney had typical kin lesions of tuberous sclerosis. Orie had been on long-term dialysis for chronienal failure due to an angiomyolipomatous lesions and the other had undergone nephrectomy because of nonfunction kidney. Hepatic hamartomas were also seen in both atients. We should anticipate that such masses are not infrequent with uberous sclerosis.