Joint Contracture and Radiologic Features in Mucopolysaccharidosis / 대한정형외과학회잡지
The Journal of the Korean Orthopaedic Association
;
: 825-829, 2004.
Article
Dans Coréen
| WPRIM
| ID: wpr-650407
ABSTRACT
PURPOSE:
To evaluate the clinical manifestations of contracted joints and the radiological features in mucopolysaccharidosis(MPS). MATERIALS ANDMETHODS:
From January 1996 to March 2002, 15 children from a pool of children diagnosed with MPS through a fibroblast culture and an enzyme assay, who could tolerate a large umber of examinations, underwent orthopedic physical and radiological examinations.RESULTS:
There were limitations in the abduction and internal rotation of the shoulder, extension limitation of the wrist, and internal rotation of the hip joint and flexion contractures of the elbow and DIP joints. Scoliotic deformities were all within the physiological curve. There were only three cases of a dorsolumbar kyphotic change and there were no neurological deficits due to the spinal deformities. The mean bone age was delayed compared with the mean chronological age. As the chronological age increased, the gap between the chronological age and the bone age increased.CONCLUSION:
Joint contracture, which is the most severe symptom in orthopedic aspect, was more severe in the upper extremities than in the lower extremities. The spinal deformity was relatively mild and there were no neurological problems. The bone age tended to be delayed as the chronological age increased.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Orthopédie
/
Épaule
/
Malformations
/
Poignet
/
Mucopolysaccharidoses
/
Contracture
/
Membre inférieur
/
Membre supérieur
/
Coude
/
Dosages enzymatiques
Limites du sujet:
Enfant
/
Humains
langue:
Coréen
Texte intégral:
The Journal of the Korean Orthopaedic Association
Année:
2004
Type:
Article
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