A Case of Cochlear Implantation in a Postligual Deaf Patient with Osteogenesis Imperfecta / 대한이비인후과학회지
Korean Journal of Otolaryngology - Head and Neck Surgery
;
: 289-292, 2009.
Article
Dans Coréen
| WPRIM
| ID: wpr-656740
ABSTRACT
Osteogenesis imperfecta is a systemic heritable disorder of connective tissues with the predominant manifestation of spontaneous bone fractures. It features an abnormal biosynthesis of collagen with the formation of pathologic, immature collagen, resulting in a triad of brittle bones, blue sclera and hearing impairment. A 39-year-old woman with osteogenesis imperfecta began noticing hearing loss as a teenager. At the time of her presentation, she was aided by a hearing aid, which she had been using for 25 years but had not been benefited from. Her temporal CT shows severe otospongiosis, with radiolucent bone surrounding the cochlea. The patient underwent cochlear implantation to her left ear with no postoperative complication. She has obtained significant hearing improvement after the cochlear implantation. Cochlear implantation in cases of osteogenesis imperfecta with otospongiosis appears to be extremely rare and we present this case with a review of the related literature.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Ostéogenèse
/
Ostéogenèse imparfaite
/
Otosclérose
/
Complications postopératoires
/
Sclère
/
Collagène
/
Implants cochléaires
/
Cochlée
/
Tissu conjonctif
/
Implantation cochléaire
Limites du sujet:
Adolescent
/
Adulte
/
Femelle
/
Humains
langue:
Coréen
Texte intégral:
Korean Journal of Otolaryngology - Head and Neck Surgery
Année:
2009
Type:
Article
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