A Case of Angiomatoid Fibrous Histiocytoma / 대한피부과학회지

ABSTRACT

Angiomatoid fibrous histiocytoma is a rare soft tissue tumor, occurring predominately in children and young adults, with a low grade malignant potency. This tumor should not be confused with, and is not identical to, the aneurysmal fibrous histiocytoma of skin. We reported a case of a 6-year-old female who presented with an asymptomatic 1.5 cm x 1.5 cm sized erythematous nodule on the left knee of 3 years duration. The lesion showed a cystic tumor surrounded by fibrous pseudocapule in the dermis and subcutis and lymphoplasmacytic infiltrations in the pericapsular area. The tumor consisted of fibroblast-like and histiocyte-like cells and pseudovascular cysts. Clinical and histological findings led to the final diagnosis of angiomatoid fibrous histiocytoma.