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A Case of Congenital Long QT Syndrome with Reccurent Syncope
Article de Ko | WPRIM | ID: wpr-69314
Bibliothèque responsable: WPRO
ABSTRACT
Congenital long QT syndrome (LQTS) is a disease characterized by prolongation of ventricle repolarization and by the occurrence, usually during emotional or physical stress, of life-threatening arrhythmias that lead to sudden death in most symptomatic and untreated patients. Two variants have been initially identified:the original Jervell and Lange-Nielsen syndrome of congenital deafness and autosomal recessive inheritance, and the more frequent Romano-Ward syndrome of autosomal dominant inheritance. Evidence also shows that approximately 25 to 30% of the cases are sporadic with syncope and a prolonged QT interval but without showing evidence for familial involvement. Familial and sporadic cases have been grouped under the definition of congenital long QT syndrome. We experienced a case of congenital long QT syndrome in a 13-year-old female girl. She had episodes of recurrent syncope and QT interval prolongation(QTc=0.46sec) in electrocardiogram(ECG). The ECG of her mother showed QT interval prologation(QTc=0.46sec). After applying atenolol, the QT interval returned to normal range and syncope has not occurred. We report a case of congenital long QT syndrome with a brief review of related literatures.
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Texte intégral: 1 Indice: WPRIM Sujet Principal: Troubles du rythme cardiaque / Valeurs de référence / Aténolol / Syncope / Testaments / Syndrome du QT long / Syndrome de Jervell et Lange Nielsen / Syndrome de Romano-Ward / Surdité / Mort subite Limites du sujet: Adolescent / Female / Humans langue: Ko Texte intégral: Journal of the Korean Pediatric Society Année: 2000 Type: Article
Texte intégral: 1 Indice: WPRIM Sujet Principal: Troubles du rythme cardiaque / Valeurs de référence / Aténolol / Syncope / Testaments / Syndrome du QT long / Syndrome de Jervell et Lange Nielsen / Syndrome de Romano-Ward / Surdité / Mort subite Limites du sujet: Adolescent / Female / Humans langue: Ko Texte intégral: Journal of the Korean Pediatric Society Année: 2000 Type: Article