Parry-Romberg Syndrome with Intracranial Vascular Dysplasia: A case report

ABSTRACT

Parry-Romberg syndrome is characterized by slowly progressive but self-limited atrophy of the facial subcutaneous fat, which can be followed by wasting of associated skin, cartilage, connective or ocular tissue, muscle and bone. The possible etiologies of Parry-Romberg syndrome are infection, immunological, trauma, sympathetic innervation, hereditary and cranial vascular malformation. The major features of this syndrome, which have been reported previously, are atrophy of the soft tissues on one side of the face with hyperpigmentation of the overlying skin and various neurologic findings, including migraine-type headache, trigeminal neuralgia and focal epilepsy. We describe the improvement of functional level related to Parry-Romberg syndrome in a child who presented the unilateral neurologic deficits and epilepsy with intracranial vascular dysplasia after comprehensive rehabilitative management.