A Case of Congenital Hepatic Fibrosis with Variceal Bleeding / 대한소아소화기영양학회지
Korean Journal of Pediatric Gastroenterology and Nutrition
;
: 98-101, 2004.
Article
Dans Coréen
| WPRIM
| ID: wpr-74110
ABSTRACT
Congenital hepatic fibrosis is an inherited, congenital disorder of the liver characterized by portal hypertension and hepatic fibrosis. We experienced a case of congenital hepatic fibrosis with esophageal varix in a 9-year-old male. He complained hematemesis, hematochezia, dizziness. In laboratory examination, AST/ALT was slightly increased. Esophageal varix was noted by an endoscopic examination. Hepatosplenomegaly and hypoechoic lesion of periportal area were seen by abdominal CT scanning. Histologic finding of liver biopsy showed fibrous tracts containing dilated bile ductules connecting adjacent portal spaces that were widened by mature fibrosis. Endocopic sclerotherpy and ligation was done. We summarized a case with review of literatures.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Bile
/
Biopsie
/
Fibrose
/
Varices oesophagiennes et gastriques
/
Tomodensitométrie
/
Hématémèse
/
Sensation vertigineuse
/
Hémorragie gastro-intestinale
/
Hypertension portale
/
Ligature
Limites du sujet:
Enfant
/
Humains
/
Mâle
langue:
Coréen
Texte intégral:
Korean Journal of Pediatric Gastroenterology and Nutrition
Année:
2004
Type:
Article
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