Chylous Manifestations and Management of Gorham-Stout Syndrome / 대한흉부외과학회지
The Korean Journal of Thoracic and Cardiovascular Surgery
;
: 44-46, 2019.
Article
Dans Anglais
| WPRIM
| ID: wpr-742333
ABSTRACT
Gorham-Stout disease (GSD) was first described by Gorham and colleagues in 1954, but its precise mechanism and cause remain to be elucidated. In this condition, voluminous and potentially fatal chylous effusions into the thorax can occur. Herein, we describe a case of GSD in which the patient presented with massive pleural effusions and mottled osteolytic bone lesions. We performed multiple operations, including thoracic duct ligation using video-assisted thoracoscopic surgery and thoracotomic decortication, but these procedures did not succeed in preventing recurrent pleural effusion and chest wall lymphedema. After administering sirolimus (0.8 mg/m2, twice a day) and propranolol (40 mg, twice a day), the process of GSD in this patient has been controlled for more than 2 years.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Épanchement pleural
/
Propranolol
/
Conduit thoracique
/
Thorax
/
Ostéolyse essentielle
/
Chylothorax
/
Sirolimus
/
Chirurgie thoracique vidéoassistée
/
Paroi thoracique
/
Ligature
Limites du sujet:
Humains
langue:
Anglais
Texte intégral:
The Korean Journal of Thoracic and Cardiovascular Surgery
Année:
2019
Type:
Article
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