Treatment of Hidradenitis Suppurativa Patient with Klinefelter Syndrome by Adalimumab
Annals of Dermatology
;
: 446-449, 2019.
Article
Dans Anglais
| WPRIM
| ID: wpr-762351
ABSTRACT
Hidradenitis suppurativa (HS) is a chronic, inflammatory and painful skin disease with recurrent nodules and tracts involving the intertriginous regions. It is known that the patient with HS shows an increased risk of metabolic disorders such as diabetes, metabolic syndrome and autoimmune diseases. Klinefelter syndrome (KS) is a sex chromosomal disorder occurring in males due to an abnormality of sexual differentiation, characterized by 47, XXY karyotype. Also, KS is related with somatic comorbidities such as metabolic syndrome, autoimmune and rheumatologic disorders as HS is. We report a HS patient with KS who shows a big improvement while on tumor necrosis factor-alpha inhibitor treatment.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Différenciation sexuelle
/
Maladies de la peau
/
Maladies auto-immunes
/
Comorbidité
/
Facteur de nécrose tumorale alpha
/
Hidrosadénite
/
Hidrosadénite suppurée
/
Maladies chromosomiques
/
Caryotype
/
Adalimumab
Limites du sujet:
Humains
/
Mâle
langue:
Anglais
Texte intégral:
Annals of Dermatology
Année:
2019
Type:
Article
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