Treatment of Keratocystic Odontogenic Tumors in Nevoid Basal Cell Carcinoma Syndrome
Journal of the Korean Association of Maxillofacial Plastic and Reconstructive Surgeons
;
: 7-12, 2014.
Article
Dans Anglais
| WPRIM
| ID: wpr-785261
ABSTRACT
Nevoid basal cell carcinoma syndrome (NBCCS) is inherited as an autosomal dominant trait with variable conditions, including multiple basal cell carcinoma, numerous keratocystic odontogenic tumors (KOTs) in the jaws, ectopic calcification of the falx cerebri, bifid ribs, macrocephaly, kyphoscoliosis, cleft palate, frontal and temporal bossing, mild ocular hypertelorism, mild mandibular prognathism, vertebral fusion, and so on. A 16-year-old boy visited the Dong-A University Medical Center, requiring diagnosis and treatment of multiple cystic lesions. He presented with many conditions related to NBCCS, including multiple KOTs, bifid rib, cleft lip, frontal bossing, mild ocular hypertelorism, and mild mandibular prognathism. No characteristic cutaneous manifestations (nevoid basal cell carcinoma) were observed in this patient. We report on a case of multiple KOTs associated with NBCCS with a review of the literature.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Prognathisme
/
Côtes
/
Carcinome basocellulaire
/
Naevomatose basocellulaire
/
Kystes odontogènes
/
Tumeurs odontogènes
/
Bec-de-lièvre
/
Fente palatine
/
Diagnostic
/
Centres hospitaliers universitaires
Type d'étude:
Etude diagnostique
Limites du sujet:
Adolescent
/
Humains
/
Mâle
langue:
Anglais
Texte intégral:
Journal of the Korean Association of Maxillofacial Plastic and Reconstructive Surgeons
Année:
2014
Type:
Article
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