Cranioplasty Using a Modified Split Calvarial Graft Technique in Cleidocranial Dysplasia
Journal of Korean Neurosurgical Society
;
: 79-82, 2015.
Article
Dans Anglais
| WPRIM
| ID: wpr-83148
ABSTRACT
Cleidocranial dysplasia is a well-documented rare autosomal dominant skeletal dysplasia characterized by hypoplastic/aplastic clavicles, brachycephalic skull, patent sutures and fontanelles, midface hypoplasia, and abnormalities of dentition. Patients with cleidocranial dysplasia often complain about undesirable esthetic appearance of their forehead and skull. Notwithstanding many studies of molecular, genetics and skeletal abnormalities of this congenial disorder, there have been very few written reports of cranioplasty involving cleidocranial dysplasia. Thus, we report a rare case of successful cranioplasty using a modified split calvarial graft technique in patient with cleidocranial dysplasia.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Crâne
/
Matériaux de suture
/
Clavicule
/
Dysostose cleido-crânienne héréditaire
/
Transplants
/
Denture
/
Front
/
Génétique
Limites du sujet:
Humains
langue:
Anglais
Texte intégral:
Journal of Korean Neurosurgical Society
Année:
2015
Type:
Article
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