Renal Cell Carcinoma Associated with Von Hippel-Lindau Disease Treated by Wedge Resection / 대한비뇨기과학회지

ABSTRACT

The Von Hippel-Lindau disease is an autosomal dominant condition manifested by the cerebellar hemangioblastomas, retinal angiomas, cysts of the pancreas, the kidney, and the epididymis, pheochromocytoma, and renal cell carcinoma. Renal cell carcinoma occurs in 35% to 38% of affected individuals and may cause pain or a palpable mass. We report a case of a 45-year-old female with renal cell carcinoma, cerebellar hemangioblastoma, and cysts of the pancreas and kidney, to which a wedge resection was performed.