A Case of Congenital Aniridia

ABSTRACT

Aniridia, a condition which shows only an extremely rudimentary iris, is a re latively rare congenital anomaly. It is almost bilateral and occurs as an autosomal dominant trait. The authors experienced one patient who had congenital aniridia combined with cataract, ectopia lentis, lens coloboma, corneal opacity and nystagmus in both eye. Intracapsular cataract extraction was performed with satisfactory result. The authors report this case with the review of literatures.