Infantile cortical hyperostosis (caffeys disease): report of a case

ABSTRACT

A 5 month old child is reported, who for 2 months presented non-hyperemic swellings over both angles of the mandible and cheeks, giving a moon-shaped face. Other manifestations were tender fusiform swellings of the right forearm and extreme irritabilityThe condition was undiagnosed for 2 months in spite of observations in 3 hospitals and consultations with several physiciansOne close observation, at the Childrens Memorial Hospital, this case presented the features, course and X-ray findings characteristic of Infantile Cortical HyperostosisThe patient improved on the 15th day in the latter hospital at which time his therapy were phenobarbital and vitaminsPersistence of the swelling prompted the use of steriod, and further improvement was apparent thereafter. This case alone cannot justify attributing favorable results to steroid therapy. (Summary)