Functional outcome of Hirchsprung's disease, post-surgical trans-anal endorectal pull-through at National Children's Hospital

ABSTRACT

BACKGROUND@#Hirschprung's Disease, is a congenital illness secondary to lack of ganglion cells in the intestinal tract leading to mechanical obstruction. In the Philippines, Hirschsprung's Disease ranks 9th over the top 10 cases causing morbidity to Filipino children and the mortality rate can reach up to 50%. The treatment is still surgery, such as Soave procedure.@*DESIGN@#Descriptive cross sectional study.@*SUBJECTS@#The participants of the study were follow up patients at the Surgery Out Patient Department from March 2016 to August 2017, ages 0-7 years old, diagnosed with Hirschsprung's Disease, post Trans-anal endorectal pull-through.@*METHODOLOGY@#Purposive sampling was used to select participants. Sample size was 40 based on the proportion of good functional outcome among patients who underwent trans-anal endorectal pull-through.@*STATISTICAL ANALYSIS@#Descriptive Analysis using proportion and percentages were used to present the results in all the variables.@*RESULTS@#Out of the 40, 82 % were diagnosed with the disease as early as the newborn period and 55% of the patients were operated at an age from 1 to 3 years old and about 80% were males. It also showed that post operatively, 60% had normal z scores and 65% of the population still had an abnormal stool. Moreover, the study showed that 95% of the subjects returned to schooling or playing post surgery.@*SUMMARY/CONCLUSION@#Comparing it to the 96% result of Dela Merced 2003, this study had 95% of patients who were able to achieve good functional outcome, 4-6 weeks post-surgery.