A Case of a Pulmonary Arteriovenous Malformation With Ebstein's Anomaly
Korean Circulation Journal
;
: 684-686, 2010.
Article
Dans Anglais
| WPRIM
| ID: wpr-98799
ABSTRACT
A pulmonary arteriovenous malformation (PAVM) is a rare pulmonary vascular anomaly presenting as dyspnea or recurrent epistaxis. Ebstein's anomaly (EA), a congenital cardiac malformation, is also a rare condition. There have been no reports concerning the co-existence of PAVM with hereditary hemorrhagic telangiectasia (HHT) and EA. A 40-year-old woman was admitted with a 2-month history of increasing dyspnea and several years of recurrent epistaxis. On transthoracic echocardiography, she was diagnosed with EA and agreed to undergo surgical treatment. A chest CT angiography showed a 12-mm serpiginous vascular structure suspicious for a PAVM and a liver CT suggested HTT. Although it is unclear whether or not a concurrent PAVM and EA have an embryologic or genetic relationship, we report a case of a PAVM with EA. Further genetic and embryonic studies are needed to identify a possible relationship of the two medical conditions.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Malformations artérioveineuses
/
Télangiectasie hémorragique héréditaire
/
Thorax
/
Angiographie
/
Échocardiographie
/
Épistaxis
/
Dyspnée
/
Maladie d'Ebstein
/
Foie
/
Poumon
Limites du sujet:
Adulte
/
Femelle
/
Humains
langue:
Anglais
Texte intégral:
Korean Circulation Journal
Année:
2010
Type:
Article
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