A new surgical procedure for treatment of total colonic aganglionosis (TCA)

ABSTRACT

Under the specific environmental circumstances of a normal developing country, a surgical procedure can save patients born with Total Colonic Aganglionosis. This new one-stage procedure comprises preservation of the ileocaecal valve, partial colon resection and a long ileum patch of the remaining colon and rectum. Normal stool habits were established due to enhanced absorption function of the remaining colon. Normal growth etc. were also noted due to adequate transit time of nutrients in the small intestine. Long-term enterostomy is difficult to manage in any depressed economy and the little ones succumb easily to malabsorption syndrome. So far two patients have benefited from this procedure. One is now 8 years, while the other is 4 years old, 6 years, and over 2 years respectively after definitive surgery