Recurrent Hyperammonemia After Abernethy Malformation Type 2 Closure: a Case Report
Ann. hepatol
;
16(3): 460-464, May.-Jun. 2017. graf
Artigo
em Inglês
| LILACS
| ID: biblio-887259
ABSTRACT
ABSTRACT The Abernethy malformation is a rare congenital malformation defined by the presence of an extrahepatic portosystemic shunt. Although most patients are asymptomatic, clinical encephalopathy is present in 15% of cases. We present a patient with type 2 Abernethy malformation, hyperammonemia, and encephalopathy. Shunt closure was performed successfully using interventional angiography; however, hyperammonemia recurred 3 months later. The diagnosis of Abernethy malformation can be made easily, but the ideal patient management strategy has not yet been established. This is the first reported patient with recurrence of hyperammonemia after interventional treatment; we discuss the therapeutic options for Abernethy malformation.(AU)
Texto completo:
DisponíveL
Índice:
LILACS (Américas)
Assunto principal:
Anormalidades Congênitas
/
Encefalopatias
/
Hiperamonemia
Limite:
Humanos
Idioma:
Inglês
Revista:
Ann. hepatol
Assunto da revista:
Gastroenterologia
Ano de publicação:
2017
Tipo de documento:
Artigo
País de afiliação:
China
Instituição/País de afiliação:
China Medical University/CN
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