Spontaneous bilateral chylothorax with fatal outcome in a patient with melorheostosis
Saudi Medical Journal. 2008; 29 (11): 1666-1668
em Inglês
| IMEMR
| ID: emr-103055
ABSTRACT
We report a case of progressive, multifocal melorheostosis in a 28-year-old woman, with involvement of the left arm, chest, spine, and impressive soft tissue involvement. In the past, she had undergone multiple vascular interventions. She presented with spontaneous massive bilateral chylothorax. After conservative treatment without success, we conducted bilateral pleurodesis. This resulted in a clear reduction of pleural effusions, but her medical condition subsequently worsened due to progressive parenchymatous infiltrates, and increased interlobal pleural effusions. She ultimately died of global respiratory insufficiency. In patients with melorheostosis, involvement of the soft tissue can result in distinctive morbidity, and whenever possible, treatment should be conservative
Buscar no Google
Índice:
IMEMR (Mediterrâneo Oriental)
Assunto principal:
Insuficiência Respiratória
/
Ducto Torácico
/
Mortalidade
/
Quilotórax
/
Evolução Fatal
/
Pleurodese
/
Malformações Vasculares
/
Melorreostose
Tipo de estudo:
Relato de Casos
Limite:
Feminino
/
Humanos
Idioma:
Inglês
Revista:
Saudi Med. J.
Ano de publicação:
2008
Similares
MEDLINE
...
LILACS
LIS