[Primary Immuno-deficiencies [PID]]

ABSTRACT

Primary immune-deficiencies [PID] are associated with a wide range of clinical disorders along with variable symptoms. The aim of this study was to evaluate and improve our knowledge regarding PID from patients that were referred to Booali Sina Hospital. We evaluated all of PID's that were referred to Booali Sina Hospital from their data records. Demography, clinical and laboratory data were recorded and then analyzed. In the duration of 3 years, we had 10 patients with PID [7 males and 3 females]. Of these cases, 5 had hum oral [50%], 1case had phagocytic [10%], 3 cases had cellular [30%] and 1 case had hyper IgE syndrome [10%]. Many of them had respiratory and otitis media infections, while a few patients had adenitis, gastroenteritis, liver abscesses, bleedings and malignancy. PID is a diverse disorder that involves different immune systems. Knowledge from patient's clinical symptoms and consideration in their differential diagnosis can be helpful in early diagnosis and an effective treatment