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Thrombotic thrombocytopaenic purpura in a patient presenting with sickle cell -hemoglobin S disease vaso-occlusive crises and acute chest syndrome
Biomedica. 2013; 29 (Jan.-Mar.): 32-36
em Inglês | IMEMR | ID: emr-143159
ABSTRACT
The association of sickle cell disease [SCA] vaso-occlusive crises and Thrombotic thrombocytopaenic purpura [TTP] has been rarely described. Here we report a case of sickle cell - haemoglobin S disease [HbSS] in which a patient presented with painful vaso-occlusive crises and acute chest syndrome and TTP which was a diagnostic challenge. We also conducted a Medline search to review reported cases previously
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Índice: IMEMR (Mediterrâneo Oriental) Assunto principal: Doenças Vasculares / Síndrome Torácica Aguda / Anemia Falciforme Tipo de estudo: Relato de Casos Limite: Humanos / Masculino Idioma: Inglês Revista: Biomedica Ano de publicação: 2013

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Índice: IMEMR (Mediterrâneo Oriental) Assunto principal: Doenças Vasculares / Síndrome Torácica Aguda / Anemia Falciforme Tipo de estudo: Relato de Casos Limite: Humanos / Masculino Idioma: Inglês Revista: Biomedica Ano de publicação: 2013