Intra-abdominal desmoplastic small round cell tumor

ABSTRACT

Intra-abdominal desmoplastic small round cell tumor [IDSRCT] is a unique, highly aggressive neoplasm that chiefly affects male adolescents and young adults and most frequently presents as a large abdominal mass with widespread peritoneal involvement at the time of diagnosis. We present two cases of IDSRCT in a young male and a female. Both typically presented with diffuse peritoneal involvement