Naevus of Ota with port wine stain - a rare entity

ABSTRACT

Nevus of Ota, which was originally described by Ota and Tanino in 1939, is a hamartoma of dermal melanocytes. It, also known as nevus fuscoceruleus ophthalmomaxillaris, is a pigmentary change involving the first and second divisions of the trigeminal nerve. Patients with the nevus of Ota have increased amounts of melanin [pigment] and melanin producing cells [melanocytes]. The melanocytosis also affects the oral cavity, nasal mucosa, external auditory canal, tympanic membrane, orbital fissures, meninges and the brain. A port-wine stain [PWS] is defined as a macular telangiectatic patch [CM] which is present at birth and persists throughout life. They may be localized or extensive, affecting a whole limb. Here, we report a rare case of co-existence of nevus of Ota and port-wine stain