[Congenital insensitivity to pain]

ABSTRACT

Congenital insensitivity to pain is rare hereditary sensory neuropathy which was first described by Deaborn in 1930. It usually manifestated in childhood by a history of unrecognized trauma, in difference to clinical features are stereotyped but its exact nosological status remains in doubt. We report two cases diagnosed with congenital insensivity to pain. These children present self-mutilations of fingers and tips, with cutaneous windys and chronic ulcerations. The diagnosis is usually delayed because of the disease's rarity and difficulties in communicating with the child because of his or her mental retardation. Management includes early recognition of the condition, prevention of injury, immobilization of extremities, and surgical correction of established deformities