Acrodermatite enteropathique

ABSTRACT

Acrodermatitis enteropathica is an inherited rare disease resulting in a disorder of zinc metabolism. Authors report a case of acrodermatitis enteropathitis enteropathica in a 6 months old infant. Typical cutaneous and mucosal lesions, diarrhea and brother's death in similar circunstances allowed the diagnosis which was confirmed by the serum zinc level. The outcome was good under zinc oral supplementation