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Currarino's syndrome
Maroc Medical. 2002; 24 (4): 262-266
em Francês | IMEMR | ID: emr-60040
ABSTRACT
Currarino's triad is a congenital malformation involving the combination of anorectal stenosis, a presacral mass and an anterior sacral bony defect. A new case is reported in a male neonate, who developed intestinal obstruction on the second day of life. The examination revealed a high anorectal malformation. A colostomy was performed. Partial agenesis of the sacrum was diagnosed radiologically. Computed tomographic myelography demonstated an anterior sacral meningocele and a tethered spinal cord. Excision of the meningocele and untethering of a tethered spinal cord were performed. Secondly, posterior sagittal anorectoplasty was performed. Colostomy was closed 3 months after rectal dilatations. Early diagnosis and management is recommended to avoid the high mortality and morbidity associated with this condition
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Índice: IMEMR (Mediterrâneo Oriental) Assunto principal: Canal Anal / Doenças do Ânus / Doenças Retais / Reto / Síndrome / Doenças do Recém-Nascido Tipo de estudo: Estudo de rastreamento Limite: Humanos / Masculino Idioma: Francês Revista: Maroc Med. Ano de publicação: 2002

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Índice: IMEMR (Mediterrâneo Oriental) Assunto principal: Canal Anal / Doenças do Ânus / Doenças Retais / Reto / Síndrome / Doenças do Recém-Nascido Tipo de estudo: Estudo de rastreamento Limite: Humanos / Masculino Idioma: Francês Revista: Maroc Med. Ano de publicação: 2002