Dysplastic gangliocytoma of the cerebellum

ABSTRACT

The authors report a case of Lhermitte-Duclos disease [Dysplastic gangliocytoma of the cererbellum] in a child, revealed by symptoms of raised intracranial pressure and diagnosed preoperatively by magnetic resonance imaging. The diagnosis of Lhermitte-Duclos disease was confirmed by histological study of the surgical specimen. Clinical imaging and pathological features of this rare entity are discussed, the literature regarding this disease is also reviewed