Multiple mucoceles in cystic fibrosis and Role of endoscopic sinus surgery in its treatment

ABSTRACT

Cystic Fibrosis [CF] is a hereditary disorder of mucous glands which due to impairment of sodium and chloride secretion affects mucosal surfaces. Although sinonasal complaints are common in CF patients, it presents usually as sinusitis or nasal polyposis and mucocele formation is a rare presentation of CF. Here we present a six year-old boy presenting with telecanthus and progressive nasal deformity as a result of multiple mucoceles in ethmoid, maxillary and sphenoid sinuses. This article discuss about this patient and reviews the role of endoscopic sinus surgery in CF patients