[Pulmonary alveolar proteinosis in two siblings. A case report]
Tunisie Medicale [La]. 2005; 83 (8): 488-491
em Francês
| IMEMR
| ID: emr-75401
ABSTRACT
Pulmonary alveolar proteinosis [PAP] is a rare disorder in children. This report describes two siblings in whom PAP developed during infancy [three years for the boy and four years two months for the girl]. The girl was admitted for chronic respiratory distress. Chest x-ray showed a reticulonodular pattern. Her brother was asymptomatic. The diagnosis of PAP was confirmed by open lung biopsy for the boy and broncho-alveolar lavage for the girl. Therapeutic broncho-alveolar lavages were performed [six for the girl and two for the boy], the girl lost dependence on oxygen therapy. 6 years later, the brother is still asymptomatic. The sister had two episodes of respiratory distress, after two and four years, that required therapeutic lavages. The last therapeutic broncho-alveolar lavage was performed for the first time by a Tunisian team
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Índice:
IMEMR (Mediterrâneo Oriental)
Assunto principal:
Insuficiência Respiratória
/
Pré-Escolar
/
Lavagem Broncoalveolar
Tipo de estudo:
Relato de Casos
Limite:
Feminino
/
Humanos
/
Masculino
Idioma:
Francês
Revista:
Tunisie Med.
Ano de publicação:
2005
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