Hemophagocytic lymphohistiocytosis in a neonate with cutis marmorata telangiectatica congenita
Saudi Medical Journal. 2006; 27 (11): 1751-1753
em Inglês
| IMEMR
| ID: emr-80659
ABSTRACT
In this case report we describe the first case of hemophagocytic lymphohistiocytosis with concurrent cutis marmorata telangiectatica congenita. She had pancytopenia and hepatosplenomegaly, hemophagocytic cells in spleen necropsy, and she died with respiratory failure and pseudomonas induced septicemia
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Índice:
IMEMR (Mediterrâneo Oriental)
Assunto principal:
Pele
/
Telangiectasia
/
Medula Óssea
/
Dermatopatias Vasculares
/
Linfo-Histiocitose Hemofagocítica
Tipo de estudo:
Relato de Casos
Limite:
Feminino
/
Humanos
Idioma:
Inglês
Revista:
Saudi Med. J.
Ano de publicação:
2006
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