Intraocular vascular tumors

ABSTRACT

It is important to distinguish between uveal and retinal vascular tumors. Choroidal hemangiomas are benign hamartomatous disorders and are classified as circumscribed or diffuse. Circumscribed tumors occur sporadically, without any associated local or systemic anomalies. In contrast, a diffuse choroidal hemangioma is usually evident at birth and generally occurs as a part of neuro-oculo-cutaneous hemangiomatosis [Sturge-Weber syndrome]. Retinal vascular tumors include capillary hemangioma, cavernous hemangioma, arteriovenous communications [Wyburn-Mason syndrome], and vasoproliferative tumor. Each subtype has a characteristic clinical feature and an attempt should be made to differentiate them because of specific systemic associations, treatment, and prognosis associated with them