Pulmonary langerhans cell histiocytosis presenting as simultaneous bilateral spontaneouse pneumothorax in a non-smoker patient
Acta Medica Iranica. 2008; 46 (3): 269-272
em Inglês
| IMEMR
| ID: emr-85609
ABSTRACT
Pulmonary Langerhans Cell Histiocytosis [PLCH] is a rare idiopathic disorder that primarily affects young adult cigarette smokers. Affected patients often present with cough and dyspnea and about 20% of patients present with or later develop pneumothorax. It is striking that more than 90% of patients are smokers. We report a very unusual case of PLCH in a 20-year- old male patient with no smoking history in whom a life- threatening complication such as simultaneous bilateral pneumothorax was the presenting feature. The final diagnosis was made by open surgical biopsy and recurrent pneumothoraces necessitated surgical management with pleurodesis. We emphasize the early use of pleurodesis in managing patients with PLCH and spontaneous pneumothorax
Buscar no Google
Índice:
IMEMR (Mediterrâneo Oriental)
Assunto principal:
Pleurodeles
/
Pneumotórax
/
Biópsia
/
Histiocitose de Células de Langerhans
Tipo de estudo:
Relato de Casos
Limite:
Humanos
/
Masculino
Idioma:
Inglês
Revista:
Acta Med. Iran.
Ano de publicação:
2008
Similares
MEDLINE
...
LILACS
LIS