Cystic adenomatoid malformation: Unusual cause of neonatal respiratory distress

ABSTRACT

Cystic adenomatoid malformation is a unilateral hamartomatous lesion that generally presents as marked respiratory distress within the first days of life. This disorder account for 95% of cases of congenital cystic lung disease. We report on a newborn male baby, a product of normal vaginal delivery following uneventful, full term pregnancy born to a healthy, multigravida Jordanian mother. The baby was admitted to neonatal intensive care unit immediately after delivery with respiratory distress. Chest ultrasound revealed a multicystic fluid filled mass lesion in the right lower lobe consistent with the diagnosis of adenomatoid malformation later confirmed by histopathology. The baby underwent surgical excision of the mass lesion that was confined to the right lower lobe. The baby did very well postoperatively and was discharged home in good condition; he is now two years old healthy, asympytomatic and growing normally. Evidence indicates long term prognosis, depending on the amount of normal lung tissue left after surgical resection, is generally good