Chediak-higashi syndrome
Pakistan Journal of Medical Sciences. 2008; 24 (2): 328-330
em Inglês
| IMEMR
| ID: emr-89517
ABSTRACT
Chediak Higashi Syndrome is a rare inherited autosomal recessive disorder of immune system. Susceptibility to infection due to phagocyte dysfunction ranges from recurrent skin infection to over whelming fatal systemic infection. A five years old male child was admitted on 31st March 2006 with the complaints of pallor, fever and ear discharge for 6 month. He was treated by several medications but had temporary relief. The ear discharge was bilateral, foul smelling and of yellowish color. Past history was significant with episodes of abscess involving the different parts of body. Myeloid precursors shows giant, purple stained granules mainly in metamyelocytes, band cells and mature neutrophils
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Índice:
IMEMR (Mediterrâneo Oriental)
Assunto principal:
Recidiva
Tipo de estudo:
Relato de Casos
Limite:
Humanos
/
Masculino
Idioma:
Inglês
Revista:
Pak. J. Med. Sci.
Ano de publicação:
2008
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