Estenose das veias pulmonares. Apresentação de dois casos e revisão da literatura / Pulmonary Vein Stenosis. Report of Two Cases and Review of the Literature
Arq. bras. cardiol
;
65(1): 47-53, Jul. 1995. ilus
Artigo
em Português
| LILACS
| ID: lil-321717
ABSTRACT
Topical congenital pulmonary vein stenosis is a uncommon defect, both isolated or associated to other cardiac abnormalities. Only the localization of the lesions seems to affect the survival, because 60 of survival cases has unilateral stenosis; the severity of associated cardiac lesions become the prognosis poor. We describe two cases 1st case, a 43 days old boy presented with heart failure and convulsion and had a diagnosis of pulmonary hypertension, atrial septal defect and tricuspid regurgitation, without pulmonary abnormalities. He had recurrent pulmonary infections and a cerebral ischemia in the following months, and died at 15 months of age for sepsis. Autopsy revealed stenosis and atresia in all pulmonary veins, with venous and arterial hypertension. There was also aortic hypoplasia and aortic and tricuspid valves indifferentiation; 2nd case, a 7 days old girl had a diagnosis of aortic coarctation and atrial and ventricular septal defects. Surgical corrections, at 38 and 46 days old, firstly of the aortic coarctation and after for the septal defects, disclosed and relief a supra-valvar mitral stenosis, but she remained on heavy respiratory insufficiency. At 6 months old, she returned to the hospital with dyspnea and cianosis, heart failure and hemoptisis; a sepsis developed and she died. At autopsy, there were severe pulmonary vein stenosis on the left and in the superior right veins, with pulmonary hypertension and hemorrhage.
Texto completo:
DisponíveL
Índice:
LILACS (Américas)
Assunto principal:
Veias Pulmonares
/
Pneumopatia Veno-Oclusiva
/
Cardiopatias Congênitas
Tipo de estudo:
Estudo prognóstico
Limite:
Feminino
/
Humanos
/
Lactente
/
Masculino
/
Recém-Nascido
Idioma:
Português
Revista:
Arq. bras. cardiol
Assunto da revista:
Cardiologia
Ano de publicação:
1995
Tipo de documento:
Artigo
País de afiliação:
Brasil
Instituição/País de afiliação:
Instituto Dante Pazzanese de Cardiologia/BR
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