Central pontine and extrapontine myelinolysis: report of a case with a tragic outcome
J. pediatr. (Rio J.)
;
82(2): 157-160, Mar.-Apr. 2006. ilus, graf
Artigo
em Inglês
| LILACS
| ID: lil-428497
ABSTRACT
OBJECTIVE: To report a pediatric case of central pontine and extrapontine myelinolysis, a rare neurological disease often associated with rapid correction of hyponatremia.DESCRIPTION: A 15 year-old female adolescent developed locked-in syndrome during severe hyponatremia. Brain magnetic resonance imaging was consistent with the diagnosis of central pontine and extrapontine myelinolysis.COMMENTS: Serum sodium correction should proceed slowly and cautiously, based upon a careful calculation of sodium deficit, in order to minimize metabolic stress and avoid the occurrence of this dreadful complication, which has a tragic outcome in most cases. There is no scientifically proved effective treatment for myelinolysis, and severe cases usually have a dismal prognosis.
Texto completo:
DisponíveL
Índice:
LILACS (Américas)
Assunto principal:
Mielinólise Central da Ponte
/
Hiponatremia
Tipo de estudo:
Estudo de etiologia
/
Estudo prognóstico
Limite:
Adolescente
/
Feminino
/
Humanos
Idioma:
Inglês
Revista:
J. pediatr. (Rio J.)
Assunto da revista:
Pediatria
Ano de publicação:
2006
Tipo de documento:
Artigo
País de afiliação:
Brasil
Instituição/País de afiliação:
Clínica Multi-Imagem Ressonância Magnética/BR
/
Universidade Federal Fluminense/BR
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