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Incontinentia pigmenti
Poziomczyk, Claudia Schermann; Recuero, Julia Kanaan; Bringhenti, Luana; Maria, Fernanda Diffini Santa; Campos, Carolina Wiltgen; Travi, Giovanni Marcos; Freitas, Andre Moraes; Maahs, Marcia Angelica Peter; Zen, Paulo Ricardo Gazzola; Fiegenbaum, Marilu; Almeida, Sheila Tamanini de; Bonamigo, Renan Rangel; Bau, Ana Elisa Kiszewski.
  • Poziomczyk, Claudia Schermann; Porto Alegre Health Sciences Federal University. Pathology Post-graduation Program. Porto Alegre. BR
  • Recuero, Julia Kanaan; Porto Alegre Health Sciences Federal University. Pathology Post-graduation Program. Porto Alegre. BR
  • Bringhenti, Luana; Porto Alegre Health Sciences Federal University. Pathology Post-graduation Program. Porto Alegre. BR
  • Maria, Fernanda Diffini Santa; Porto Alegre Health Sciences Federal University. Pathology Post-graduation Program. Porto Alegre. BR
  • Campos, Carolina Wiltgen; Porto Alegre Health Sciences Federal University. Pathology Post-graduation Program. Porto Alegre. BR
  • Travi, Giovanni Marcos; Porto Alegre Health Sciences Federal University. Pathology Post-graduation Program. Porto Alegre. BR
  • Freitas, Andre Moraes; Porto Alegre Health Sciences Federal University. Pathology Post-graduation Program. Porto Alegre. BR
  • Maahs, Marcia Angelica Peter; Porto Alegre Health Sciences Federal University. Pathology Post-graduation Program. Porto Alegre. BR
  • Zen, Paulo Ricardo Gazzola; Porto Alegre Health Sciences Federal University. Pathology Post-graduation Program. Porto Alegre. BR
  • Fiegenbaum, Marilu; Porto Alegre Health Sciences Federal University. Pathology Post-graduation Program. Porto Alegre. BR
  • Almeida, Sheila Tamanini de; Porto Alegre Health Sciences Federal University. Pathology Post-graduation Program. Porto Alegre. BR
  • Bonamigo, Renan Rangel; Porto Alegre Health Sciences Federal University. Pathology Post-graduation Program. Porto Alegre. BR
  • Bau, Ana Elisa Kiszewski; Porto Alegre Health Sciences Federal University. Pathology Post-graduation Program. Porto Alegre. BR
An. bras. dermatol ; 89(1): 26-36, Jan-Feb/2014. tab, graf
Artigo em Inglês | LILACS | ID: lil-703556
ABSTRACT
Incontinentia pigmenti is a rare genodermatosis in which the skin involvement occurs in all patients. Additionally, other ectodermal tissues may be affected, such as the central nervous system, eyes, hair, nails and teeth. The disease has a X-linked dominant inheritance pattern and is usually lethal to male fetuses. The dermatological findings occur in four successive phases, following the lines of Blaschko First phase - vesicles on an erythematous base; second phase - verrucous hyperkeratotic lesions; third phase - hyperchromic spots and fourth phase - hypochromic atrophic lesions.
Assuntos


Texto completo: DisponíveL Índice: LILACS (Américas) Assunto principal: Pele / Incontinência Pigmentar Tipo de estudo: Estudo de etiologia Limite: Humanos / Masculino Idioma: Inglês Revista: An. bras. dermatol Assunto da revista: Dermatologia Ano de publicação: 2014 Tipo de documento: Artigo País de afiliação: Brasil Instituição/País de afiliação: Porto Alegre Health Sciences Federal University/BR

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Texto completo: DisponíveL Índice: LILACS (Américas) Assunto principal: Pele / Incontinência Pigmentar Tipo de estudo: Estudo de etiologia Limite: Humanos / Masculino Idioma: Inglês Revista: An. bras. dermatol Assunto da revista: Dermatologia Ano de publicação: 2014 Tipo de documento: Artigo País de afiliação: Brasil Instituição/País de afiliação: Porto Alegre Health Sciences Federal University/BR